Chiari malformation (Arnold-Chiari malformation) is a congenital CNS anomaly. It is a dystopia of the cerebellum and medulla oblongata into the spinal canal, which is clinically manifested by hydrocephalus. RWe distinguish four types of rhombencephalon abnormalities (cerebellum, pons, oblongata):
- Type 1 - herniation of the cerebellar tonsil under the foramen magnum, IV. the chamber is stored normally
- Type 2 - usually the co-presence of myelomeningocele
- Type 3 - severe dislocation of structures in the posterior pit, often associated with suboccipital encephalomeningocele; usually incompatible with life
- Type 4 - cerebellar hypoplasia without herniation.
Clinical picture[edit | edit source]
Clinically, the defect is manifested mainly by headache, weakened grip and spasticity of DK.
Diagnosis[edit | edit source]
Native X-ray, MRI.
Therapy[edit | edit source]
The main problem is hydrocephalus – decompression of the craniospinal junction, short-circuit drainage operations.