Eisenmenger's syndrome

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eisenmengers syndrome
Schematic picture describing the principle of Eisenmenger syndrome
Clinical picture stiffness-clubbed fingers-cyanosis
Diagnostika ECG- chest xray- ECHO
Therapy cannot be cured

Eisenmenger's syndrome is a short-circuit defect at any level (aortopulmonary, atrial, ventricular) along with secondary pulmonary hypertension. It results in the change of the original left-right short circuit to right-left.

  • Pulmonary hypertension significant;
  • pathogenesis unclear (pulmonary burden on the volume of recirculating blood);
  • media hypertrophy, fibrotization and cellular infiltration of the intima of the pulmonary branches (pulmonary vascular disease);
  • hypertrophy and right ventricular insufficiency (insufficiency of the tricuspid valve).

Clinical picture[edit | edit source]

  • Progressive dyspnea;
  • clubbed fingers;
  • cyanosis.

Diagnostics[edit | edit source]

  • Tricuspid insufficiency (prominent wave "a" on the venous pulse in the neck);
  • curious right ventricular stroke subxifoidally;
  • systolic ejection crank; systolic murmur above the lungs with emphasis II. echoes;
  • ECG: hypertrophy of the right atrium with prominence of P wave in leads II, III, aVF;
  • Chest x-ray: prominence of the pulmonary arch;
  • ECHO: presence of congenital heart disease, signs of pulmonary hypertension, consequences.

Therapy[edit | edit source]

  • Eisenmenger syndrome cannot be treated;
  • important prevention by cardiac surgery in childhood;
  • heart and lung transplantation;
  • reason for abortion for health reasons.

Links[edit | edit source]

related articles[edit | edit source]

References[edit | edit source]

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