Congenital defects of the inner ear

From WikiLectures

  • Anomalies of the inner ear are caused by disorders of otocyst formation . Different types of labyrinth hypoplasia arise due to a disorder in the development of the otocyst.

Mondini anomaly[edit | edit source]

  • A normal snail has 2.5 turns. In the case of Mondini anomaly , the cochlea has only 1 turn and there is a pathological communication between the scala vestibuli and the scala tympani with simultaneous expansion of the saccus and ductus endolymphaticus .
  • Hearing impairment varies in extent.
  • Diagnosis is mainly based on CT .

Links[edit | edit source]

Source[edit | edit source]

References[edit | edit source]

  • KLOZAR, Jan, et al. Speciální otorinolaryngologie. 1. edition. Praha : Galén, 2005. pp. 224. ISBN 80-7262-346-X.