Eisenmenger's syndrome

eisenmengers syndrome


Schematic picture describing the principle of Eisenmenger syndrome
Clinical picture	stiffness-clubbed fingers-cyanosis
Diagnostika	ECG- chest xray- ECHO
Therapy	cannot be cured

Eisenmenger's syndrome is a short-circuit defect at any level (aortopulmonary, atrial, ventricular) along with secondary pulmonary hypertension. It results in the change of the original left-right short circuit to right-left.

Pulmonary hypertension significant;
pathogenesis unclear (pulmonary burden on the volume of recirculating blood);
media hypertrophy, fibrotization and cellular infiltration of the intima of the pulmonary branches (pulmonary vascular disease);
hypertrophy and right ventricular insufficiency (insufficiency of the tricuspid valve).

Clinical picture[edit | edit source]

Progressive dyspnea;
clubbed fingers;
cyanosis.

Diagnostics[edit | edit source]

Tricuspid insufficiency (prominent wave "a" on the venous pulse in the neck);
curious right ventricular stroke subxifoidally;
systolic ejection crank; systolic murmur above the lungs with emphasis II. echoes;
ECG: hypertrophy of the right atrium with prominence of P wave in leads II, III, aVF;
Chest x-ray: prominence of the pulmonary arch;
ECHO: presence of congenital heart disease, signs of pulmonary hypertension, consequences.

Therapy[edit | edit source]

Eisenmenger syndrome cannot be treated;
important prevention by cardiac surgery in childhood;
heart and lung transplantation;
reason for abortion for health reasons.

Links[edit | edit source]

References[edit | edit source]

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