Madelung deformity

Bayonet-like attachment of the hand to the forearm: caused by volar flexion and shortening of the distal end of the radius. Clinical image: the proximal row of the carpal bones is volarly subluxated, the ulnar end of the forearm protrudes dorsally;

Etiology: this deviation occurs after some fractures and epiphysiolysis of the distal end of the radius where the growth cartilage has been damaged. .

Madelung's wrist deformity is a typical finding in Léry-Weill type of dyschondrosteosis (OMIM: 127300), conditioned by a mutation in the SHOX (or SHOXY) gene.