Binder syndrome

Synonyms: dysosteosis maxillonasalis, dysplasia maxillonasalis.

Named after the Austrian dentist Kurt Binder.


 * Genetics:
 * OMIM: 155050
 * The etiology is probably heterogeneous, if the syndrome repeats in families, then it shows autosomal dominant inheritance.


 * Characteristics:


 * flat short nose,
 * crescent shaped nostrils,
 * the base of the upper jaw is flat,
 * pseudoprogeny,
 * hypoplasia to aplasia of the sinus frontalis and the anterior nasal process of the jaw.