Eisenmenger's syndrome

Eisenmenger's syndrome is a short-circuit defect at any level (aortopulmonary, atrial, ventricular) along with secondary pulmonary hypertension. It results in the change of the original left-right short circuit to right-left.


 * Pulmonary hypertension significant;
 * pathogenesis unclear (pulmonary burden on the volume of recirculating blood);
 * media hypertrophy, fibrotization and cellular infiltration of the intima of the pulmonary branches (pulmonary vascular disease);
 * hypertrophy and right ventricular insufficiency (insufficiency of the tricuspid valve).

Clinical picture

 * Progressive dyspnea;
 * clubbed fingers;
 * cyanosis.

Diagnostics

 * Tricuspid insufficiency (prominent wave "a" on the venous pulse in the neck);
 * curious right ventricular stroke subxifoidally;
 * systolic ejection crank; systolic murmur above the lungs with emphasis II. echoes;
 * ECG: hypertrophy of the right atrium with prominence of P wave in leads II, III, aVF;
 * Chest x-ray: prominence of the pulmonary arch;
 * ECHO: presence of congenital heart disease, signs of pulmonary hypertension, consequences.

Therapy

 * Eisenmenger syndrome cannot be treated;
 * important prevention by cardiac surgery in childhood;
 * heart and lung transplantation;
 * reason for abortion for health reasons.

related articles

 * congenital heart defects
 * Congenital malformations